nasledstvennie narusheniya razvitiya tverdix tkaney zubov
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5.1.3. nasledstvennie narusheniya razvitiya tverdix tkaney zubov k nasledstvennim porokam razvitiya tverdix tkaney zubov otnosyatsya nasledstvenniy nesovershenniy amelogenez (nna), nasledstvenniy nesovershenniy dentinogenez (nnd), nasledstvenniy opalestsiruyushiy dentin (nod). nasledstvenniy nesovershenniy amelogenez (nna) otnositsya k chislu naibolee redkix i nedostatochno izuchennix porokov razvitiya tverdix tkaney zubov, imeet razlichnie formi, raznie klinicheskie proyavleniya, a takje raznie tipi nasledovaniya. v osnove etogo poroka razvitiya lejit nasledstvennoe nedorazvitie ektodermalnoy zarodishevoy tkani. nna chashe vstrechaetsya kak samostoyatelniy porok razvitiya emali, no mojet bit takje proyavleniem sochetannix sind-romnix assotsiatsiy i xromosomnix bolezney. danniy p...
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