nasledstvennie narusheniya razvitiya tverdix tkaney zubov

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5.1.3. nasledstvennie narusheniya razvitiya tverdix tkaney zubov k nasledstvennim porokam razvi​tiya tverdix tkaney zubov otnosyatsya nasledstvenniy nesovershenniy amelogenez (nna), nasledstven​niy nesovershenniy dentinogenez (nnd), nasledstvenniy opalestsiruyushiy dentin (nod). nasledstvenniy nesovershenniy amelogenez (nna) otnositsya k chis​lu naibolee redkix i nedostatochno izuchennix porokov razvitiya tver​dix tkaney zubov, imeet razlichnie formi, raznie klinicheskie proyav​leniya, a takje raznie tipi nasle​dovaniya. v osnove etogo poroka razvitiya lejit nasledstvennoe ne​dorazvitie ektodermalnoy zaro​dishevoy tkani. nna chashe vstre​chaetsya kak samostoyatelniy porok razvitiya emali, no mojet bit tak​je proyavleniem sochetannix sind-romnix assotsiatsiy i xromosomnix bolezney. danniy porok razvitiya privodit k izmeneniyu tsveta ema​li, ee istoncheniyu, umensheniyu velichini koronok, poyavleniyu na poverxnosti koronok yamok, oval​nix uglubleniy i borozdok, chto vizivaet narushenie esteticheskoy vneshnosti rebenka. vozniknovenie toy ili inoy formi nna obuslov​leno narusheniyami, proisxodyashi​mi v matritse emali. tak, razvitie gipoplasticheskoy formi svyazano s narusheniem protsessa formirova​niya matritsi emali; gipomaturatsionnoy formi — s narusheniem ee sozrevaniya, gipomineralizovannoy formi — s narusheniem ee minera​lizatsii. …
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niy prisushi svoi priznaki. gipoplasticheskaya forma nna imeet 6 vidov klinicheskix proyav​leniy. autosomno-dominantniy yamochno-borozdchatiy gipoplasticheskiy nna (ris. 5.13). priznaki: na zubax vid​ni melkie i srednie po glubine yamki i borozdki, kolichestvo koto​rix razlichno; chashe oni lokalizu​yutsya na vestibulyarnoy i shechnoy poverxnostyax koronok. v menshem kolichestve defekti viyavlyayutsya na yazichnoy, nebnoy i kontaktnoy po​verxnostyax. yamki raspolojeni xa​otichno ili vistroeni v vide pro​dolnix stolbikov, borozdki takje imeyut prodolnoe napravlenie. protyajennost vistroennix v stolbiki yamok ili borozdok biva​et neodinakovoy. na odnix zubax, nachinayas ot rejushego kraya i bug​rov, oni doxodyat do polovini ko​ronok, na drugix defekti raspola​gayutsya tolko v sredney ix chasti, reje, nachinayas ot rejushego kraya i bugrov, oni dostigayut sheyki zuba. te defekti, kotorie nachina​yutsya ot rejushego kraya i vershin bugrov, vizivayut ix istonchenie, privodyashee k obrazovaniyu skolov. sloy emali istonchen lish v mes​tax obrazovavshixsya defektov, v ko​torix za schet pishevogo pigmenta izmenen ee tsvet. pigment ne pro​nikaet v glub emali …
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oy ee istonchen lish v mestax ug​lubleniy. tsvet emali izmenen to​lko v gipoplazirovannix iston​chennix uchastkax, v kotorix ona svetlo-jeltogo ili svetlo-korich​nevogo tsveta. intensivnost okra​ski emali zavisit ot glubini de​fekta i vozrasta rebenka. chem star​she rebenok i glubje defekti, tem intensivnee okrashivaetsya iston​chennaya emal i obnajenniy den​tin. chislo porajennix molochnix i postoyannix zubov variruet. autosomno-dominantniy gipopla​sticheskiy gladkiy nna. zubi menshey velichini, pravilnoy formi, sloy emali istonchen po vsey poverxnosti koronok, tsvet ee variruet ot svetlo-jeltogo do svetlo-korichnevogo. poverxnost koronok gladkaya, blestyashaya, povi​shennoy prozrachnosti. emal do​statochno tverdaya. na nekotorix zu​bax otmecheni melkie skoli, soche​tayushiesya s patologicheskoy stiraemostyu. mejdu zubami imeyutsya tremi. otmechaetsya giperesteziya ot temperaturnix razdrajiteley. po​rajeni molochnie i postoyannie zubi. autosomno-dominantniy gipoplasticheskiy granuloobrazniy nna. na poverxnosti koronok vidni mnojestvennie yamki i borozdki, raspolagayushiesya xaotichno, imeyu​shie razlichnuyu glubinu, a posled​nie — neodinakovuyu shirinu i dli​nu. emal, naxodyashayasya mejdu yam​kami i borozdkami, granuloobraznogo vida, dostatochno tverdaya, prochno soedinyaetsya s dentinom, is​tonchena po vsey …
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noe vpechatlenie nalichiya na jevatelnoy poverxnosti zubov karioznix polostey. so vremenem shipi otkalivayutsya. na molochnix molyarax otkoli shipov chashe obna​rujivayutsya na verxushke bugrov, v tom meste, otkuda oni berut nachalo. na postoyannix zubax otkoli na​blyudayutsya s odinakovoy chastotoy, kak na vershine bugrov, v sredney ix chasti, tak i u osnovaniya. skolov​shiesya u osnovaniya bugra shipi ostavlyayut na jevatelnoy poverx​nosti uchastki obnajennogo denti​na, po kotorim mojno opredelit kolichestvo imevshixsya ranee bug​rov. deti jaluyutsya na gipereste​ziyu. obnajenniy dentin imeet ne​odinakovuyu okrasku, intensivnost kotoroy zavisit ot davnosti skola i ego glubini. nablyudaetsya poraje​nie molochnix i postoyannix zubov. x-stseplenniy dominantniy gipoplasticheskiy nna gladkiy u mujchin. emal neznachitelno is​tonchena po vsey poverxnosti koro​nok, gladkaya, blestyashaya, jeltova​to-korichnevaya na bokovix zubax i svetlo-jeltaya na perednix. otme​chayutsya tremi, patologicheskaya stiraemost emali i giperplaziya. po​rajeni molochnie i postoyannie zubi. x-stseplenniy dominantniy gipoplasticheskiy nna poloschato-bo​rozdchatiy u jenshin. na vestibu​lyarnoy i shechnoy poverxnostyax ko​ronok imeyutsya prodolno raspolo​jennie polosi i borozdi. emal …
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ema​li imeyut izmenennuyu formu i umenshennuyu velichinu. istonche​nie i skalivanie emali bolee chas​to otmechayutsya na vestibulyarnoy i shechnoy poverxnosti koronok. so​xranivshayasya emal viglyadit v vide tonkix, malenkix ostrovkov, koto​rie pri popitke otdeleniya ix ot dentina legko skalivayutsya ili ot​delyayutsya tselikom, chto ukazivaet na xrupkost emali i oslablenie ee stsepleniya s dentinom. eti ostrov​ki emali pridayut poverxnosti koronok sheroxovatost. bolee tol​stiy sloy emali otmechaetsya v prisheechnoy oblasti koronok. bolshoe kolichestvo soxranivsheysya emali obnarujivaetsya na kontaktnoy i nebnoy poverxnostyax zubov. u raz​nix grupp zubov tsvet emali neodi​nakov, on variruet ot svetlo-jel​togo na perednix zubax do tem​no-korichnevogo na jevatelnix. na bugrax molochnix i postoyannix molyarov nablyudayutsya melkie sko​li i neznachitelnaya patologiche​skaya stiraemost emali. imeyutsya tremi i giperesteziya, porajeni molochnie i postoyannie zubi. gipomaturatsionnaya forma nna imeet 4 vida klinicheskix proyavle​niy. autosomno-dominantniy gipomaturatsionniy pigmentirovanniy nna (ris. 5.14). poverxnost koro​nok v pervoe vremya posle prorezi​vaniya zubov gladkaya, tolshina ema​li v predelax normi, tremi otsut​stvuyut. emal …

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5.1.3. nasledstvennie narusheniya razvitiya tverdix tkaney zubov k nasledstvennim porokam razvi​tiya tverdix tkaney zubov otnosyatsya nasledstvenniy nesovershenniy amelogenez (nna), nasledstven​niy nesovershenniy dentinogenez (nnd), nasledstvenniy opalestsiruyushiy dentin (nod). nasledstvenniy nesovershenniy amelogenez (nna) otnositsya k chis​lu naibolee redkix i nedostatochno izuchennix porokov razvitiya tver​dix tkaney zubov, imeet razlichnie formi, raznie klinicheskie proyav​leniya, a takje raznie tipi nasle​dovaniya. v osnove etogo poroka razvitiya lejit nasledstvennoe ne​dorazvitie ektodermalnoy zaro​dishevoy tkani. nna chashe vstre​chaetsya kak samostoyatelniy porok razvitiya emali, no mojet bit tak​je proyavleniem sochetannix sind-romnix assotsiatsiy i xromosomnix bolezney. danniy p...

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