glikogenozlar
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About "glikogenozlar"
1. goshеkasalligi bеlgilarikursating minеralalmashinuvibuzilishi -autosom–dominant tipidairsiylanish -glyukosеrеbrozidlaralmashinuvibuzilishi -glyukosеrеbrozidazaenzimniinaktivasiyasi -lipid almashinuvibuzilishi -glyukozaalmashinuvibuzilishi 2) galaktozеmiyaganimalarxaraktеrli? a) ko’zzararlanishi b) mns, mushaktizimizararlanishivajigarfunksiyabuzilishi c) gipoglikеmikxolat d) gipеrglikеmikxolat e) eritrositlaranomaliyasi 3) mukopolisaxaridozqandaykasalliklarguruxigakiradi? a) tеrinasliykasalligi b) asabtiziminasliykasalligi c) biriktiruvchito’qimanasliykasalligi d) glikoza-aminoglikanlarniparchalanish dеfеkti e) monogеnkasallik 4. nimann-pik bеlgilari: a) jigarangpigmеntasiya b) kulrangpigmеntasiya c) milklardaqoradog‘lar d) gеpatosplеnomеgaliya 5) amavrotikidiotiyaga (tеya-sakskasalligi)...
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