rey sindromi
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About "rey sindromi"
rey sindromi umumiy ma’lumot - neyrometabolik, kamyob, og‘ir holat - asosan 4–12 yoshdagi bolalarda uchraydi - taxminan jigar va miya shikastlanishi bilan kechadi - tez rivojlanadigan ensefalopatiya va gepatopatiya etiologiyasi va xavf omillari - ko‘pincha virusli infektsiyalar (gripp a/b, varicella) - aspirin yoki salisilatlar bilan davolashdan keyin bog‘lanadi - genetik moyillik ba’zan rol o‘ynashi mumkin (mitoxondrial kasalliklar) patofiziologiyasi mitoxondrial disfunksiya va hujayra metabolizmi buzilishi - oksidlovchi fosforillanish inhibisyoni - xujayra darajasida laktik kislota ko‘payishi va ammiak darajasi oshishi - jigar hujayralarining nekrozi va serebral ödem hosil bo‘lishi klinik belgilari dastlabki: qusish, charchoq, irritabellik - neurologik: huşsizlik, konvulsiya, koma, mansa...
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